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The book deals with the latest research on membrane distillation. New membrane and module designs, low-temperature applications, integration with other membrane units and pilot scale investigations are presented and discussed.

FGD wastewater --- integrated membrane-based process --- zero liquid-discharge --- sustainability --- bioethanol --- sweeping gas membrane distillation --- SGMD --- glucose --- permeate flux --- optimization --- membrane distillation --- triple layer composite membrane --- highly concentrated solutions --- PVDF --- PES --- membrane stability --- polypropylene --- TIPS --- talc --- desalination --- brine treatment --- pilot scale --- permeate quality --- membrane filtration --- high salinity --- spacer-filled channel --- temperature polarization --- computational fluid dynamics --- thermochromic liquid crystals --- distillation --- high recovery rate --- brine concentration --- zero liquid discharge --- membrane distillation module --- wastewater concentration --- resource recovery --- 1,3-dimethyl-2-imidazolidinone --- solvent dehydration --- hollow-fiber membrane --- multi-objective optimization --- submerged module --- capillary membrane --- direct contact membrane distillation --- urea --- low temperature --- composite membrane --- plasma-polymerized hydrophobic fluorosiloxane coating --- hydrophilic porous hollow-fiber substrate --- n/a

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• Reference Manager
• EndNote
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The book deals with the latest research on membrane distillation. New membrane and module designs, low-temperature applications, integration with other membrane units and pilot scale investigations are presented and discussed.

Technology: general issues --- FGD wastewater --- integrated membrane-based process --- zero liquid-discharge --- sustainability --- bioethanol --- sweeping gas membrane distillation --- SGMD --- glucose --- permeate flux --- optimization --- membrane distillation --- triple layer composite membrane --- highly concentrated solutions --- PVDF --- PES --- membrane stability --- polypropylene --- TIPS --- talc --- desalination --- brine treatment --- pilot scale --- permeate quality --- membrane filtration --- high salinity --- spacer-filled channel --- temperature polarization --- computational fluid dynamics --- thermochromic liquid crystals --- distillation --- high recovery rate --- brine concentration --- zero liquid discharge --- membrane distillation module --- wastewater concentration --- resource recovery --- 1,3-dimethyl-2-imidazolidinone --- solvent dehydration --- hollow-fiber membrane --- multi-objective optimization --- submerged module --- capillary membrane --- direct contact membrane distillation --- urea --- low temperature --- composite membrane --- plasma-polymerized hydrophobic fluorosiloxane coating --- hydrophilic porous hollow-fiber substrate --- n/a

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Nephropathic cystinosis (MIM # 219800) is a rare autosomal recessive disorder caused by mutations in the lysosomal cystine transporter cystinosin, encoded by the CTNS gene (17p13.2). This devastating condition initially affects kidneys and subsequently many other organs including eyes, thyroid, pancreas, muscles, and brain. While lysosomal cystine storage is a key feature of the disease and the main target of current therapy, recent groundbreaking research has revealed that cystinosin has diverse functions in cells, being involved in vesicle trafficking, energy homeostasis, and cell death mechanisms. These discoveries deepen our insights into the mechanisms of cystinosis and of lysosomal biology in general. In this Special Issue dedicated to the pioneer of cystinosis research Dr. Jerry Schneider, we highlight the state-of-the-art understanding of cellular and molecular mechanisms of various disease features, opening new horizons for innovative treatment strategies for cystinosis and potentially other lysosomal storage diseases.

Medicine --- Pharmacology --- cystinosis --- cysteamine --- bone --- osteoclast --- genotype --- CD34+ hematopoietic stem and progenitor cells --- gene therapy --- pre-clinical studies --- investigational new drug application --- clinical trial --- disulfiram --- mice --- zebrafish --- fertility --- azoospermia --- hypogonadism --- histopathology --- mouse model --- lysosomal storage disease --- cell and animal models --- infantile nephropathic cystinosis --- bone-muscle wasting --- fibroblast growth factor 23 --- osteoclasts --- sclerostin --- leptin --- fractures --- nephropathic cystinosis --- hollow fiber membrane --- 3-dimensional models --- autophagy --- macrophages --- inflammasome --- proximal tubular cells --- endocytosis --- apoptosis --- chitotriosidase --- interleukins --- galectin-3 --- novel therapies --- endolysosome --- epithelial cell differentiation --- homeostasis --- lysosomal storage diseases --- mitochondrial distress --- kidney proximal tubule --- programmed cell death --- central nervous system --- cortical atrophy --- arterial spin labelling --- cystine blood level --- lysosomal storage disorder --- history --- treatment strategies for cystinosis --- newborn screening --- clinical course --- CTNS-pathogenic variants --- newborn screening for cystinosis --- kidney progenitors --- cell model --- biomarkers --- cystine --- kidney --- therapeutic monitoring --- cystinosis --- cysteamine --- bone --- osteoclast --- genotype --- CD34+ hematopoietic stem and progenitor cells --- gene therapy --- pre-clinical studies --- investigational new drug application --- clinical trial --- disulfiram --- mice --- zebrafish --- fertility --- azoospermia --- hypogonadism --- histopathology --- mouse model --- lysosomal storage disease --- cell and animal models --- infantile nephropathic cystinosis --- bone-muscle wasting --- fibroblast growth factor 23 --- osteoclasts --- sclerostin --- leptin --- fractures --- nephropathic cystinosis --- hollow fiber membrane --- 3-dimensional models --- autophagy --- macrophages --- inflammasome --- proximal tubular cells --- endocytosis --- apoptosis --- chitotriosidase --- interleukins --- galectin-3 --- novel therapies --- endolysosome --- epithelial cell differentiation --- homeostasis --- lysosomal storage diseases --- mitochondrial distress --- kidney proximal tubule --- programmed cell death --- central nervous system --- cortical atrophy --- arterial spin labelling --- cystine blood level --- lysosomal storage disorder --- history --- treatment strategies for cystinosis --- newborn screening --- clinical course --- CTNS-pathogenic variants --- newborn screening for cystinosis --- kidney progenitors --- cell model --- biomarkers --- cystine --- kidney --- therapeutic monitoring