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Introduction :
Le traitement chirurgical des APSI est entaché d’une mortalité lourde, liée à la grande complexité des différentes formes anatomiques.
Objectifs :
Ce travail étudie 29 nouveau-nés traités de 1980 à 1992 et évalue les facteurs influençant les résultats des différentes stratégies thérapeutiques.
Méthode
Il s’agit d’une analyse rétrospective des dossiers cliniques, angiographiques et des protocoles opératoires des patients.
Résultats :
La chirurgie néonatale (<1 mois d’âge) est faite chez 27/29 patients ; 2 enfants n’en bénéficient pas, le premier sur décision des parents et le second pour prématurité. Ce dernier survit grâce à une perfusion de prostaglandines et reçoit à un mois une anastomose aorto-pulmonaire.
Onze des 27 nouveau-nés (41%) décèdent dans les suites opératoires immédiates. La mortalité est ainsi répartie :
- connexion VD-APC isolée 6/10 (60%),
- connexion VD-APC et shunt aorto-pulmonaire 3/9 (33%),
- shunt aorto-pulmonaire isolé 1/7 (14%),
- shunt aorto-pulmonaire suivi d’une excision tricuspide 1/1.
Après la période néonatale, 13/17 (76%) des survivants (en incluant le prématuré opéré tardivement), reçoivent une seconde chirurgie. Trois patients n’ont pas été réopérés, leur état clinique n’ayant pas nécessité une intervention chirurgicale complémentaire. Un enfant est mort d’une infection respiratoire.
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Congenital heart disease. --- Heart Defects, Congenital --- Pulmonary Atresia --- Child --- Tetralogy of Fallot --- Ventricular Dysfunction, Right --- Infant --- Vascular Malformations --- Age Groups --- Ventricular Dysfunction --- Heart Diseases --- Cardiovascular Abnormalities --- Heart Valve Diseases --- Persons --- Cardiovascular Diseases --- Congenital Abnormalities --- Congenital, Hereditary, and Neonatal Diseases and Abnormalities --- Diseases --- Named Groups --- Abnormality, Heart --- Congenital Heart Defect --- Congenital Heart Defects --- Defects, Congenital Heart --- Heart Defect, Congenital --- Heart, Malformation Of --- Congenital Heart Disease --- Heart Abnormalities --- Congenital Heart Diseases --- Defect, Congenital Heart --- Disease, Congenital Heart --- Heart Abnormality --- Heart Disease, Congenital --- Malformation Of Heart --- Malformation Of Hearts --- Heart --- Myocardium --- Disorders, Congenital --- Congenital Disorders --- Neonatal Diseases and Abnormalities --- Congenital Disorder --- Disorder, Congenital --- Abnormalities, Congenital --- Defects, Congenital --- Birth Defects --- Congenital Defects --- Deformities --- Fetal Anomalies --- Fetal Malformations --- Abnormality, Congenital --- Anomaly, Fetal --- Birth Defect --- Congenital Abnormality --- Congenital Defect --- Defect, Birth --- Defect, Congenital --- Deformity --- Fetal Anomaly --- Fetal Malformation --- Malformation, Fetal --- Fetal Diseases --- Infant, Newborn, Diseases --- Teratogenesis --- Cardiovascular Disease --- Disease, Cardiovascular --- Diseases, Cardiovascular --- Cardiology --- Cardiac Diseases --- Cardiac Disorders --- Heart Disorders --- Cardiac Disease --- Cardiac Disorder --- Heart Disease --- Heart Disorder --- Dysfunction, Ventricular --- Dysfunctions, Ventricular --- Ventricular Dysfunctions --- Person --- Heart Valvular Disease --- Valvular Heart Diseases --- Disease, Heart Valvular --- Heart Disease, Valvular --- Heart Valve Disease --- Heart Valvular Diseases --- Valve Disease, Heart --- Valvular Disease, Heart --- Valvular Heart Disease --- Age Group --- Group, Age --- Groups, Age --- Abnormalities, Cardiovascular --- Abnormality, Cardiovascular --- Cardiovascular Abnormality --- Cardiovascular System --- Malformation, Vascular --- Malformations, Vascular --- Vascular Malformation --- Infants --- Right Ventricular Dysfunction --- Dysfunction, Right Ventricular --- Dysfunctions, Right Ventricular --- Right Ventricular Dysfunctions --- Ventricular Dysfunctions, Right --- Tetralogy, Fallot's --- Fallot's Tetralogy --- Fallot Tetralogy --- Fallots Tetralogy --- Tetralogy, Fallot --- Tetralogy, Fallots --- Pentalogy of Cantrell --- Children --- Minors --- Atresia, Pulmonary Valve --- Atresias, Pulmonary --- Atresias, Pulmonary Valve --- Pulmonary Atresias --- Pulmonary Valve Atresias --- Atresia, Pulmonary --- Pulmonary Valve Atresia --- Valve Atresia, Pulmonary --- Valve Atresias, Pulmonary --- abnormalities --- Adverse Cardiac Event --- Cardiac Events --- Major Adverse Cardiac Events --- Adverse Cardiac Events --- Cardiac Event --- Cardiac Event, Adverse --- Cardiac Events, Adverse --- Event, Cardiac --- Names --- Heart Defects, Congenital. --- Pulmonary Atresia. --- Child. --- Tetralogy of Fallot. --- Ventricular Dysfunction, Right. --- Infant. --- Vascular Malformations. --- Age Groups. --- Ventricular Dysfunction. --- Heart Diseases. --- Cardiovascular Abnormalities. --- Heart Valve Diseases. --- Persons. --- Cardiovascular Diseases. --- Congenital Abnormalities. --- Congenital, Hereditary, and Neonatal Diseases and Abnormalities. --- Disease. --- Names.
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