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Maladie de Creutzfeldt-Jakob et autres maladies à prion
Authors: ---
ISBN: 2257155416 9782257155412 Year: 1996 Volume: *6 Publisher: Paris : Flammarion,

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Abstract

SOMMAIRE.- Introduction.- Les encéphalopathies spongiformes transmissibles animales.- La tremblante naturelle du mouton (ou scrapie).- L'encéphalopathie spongiforme bovine ou Maladie des vaches folles.- Les autres encéphalopathies spongiformes animales.- Les encéphalopathies spongiformes transmissibles humaines.- Le Kuru.- La maladie de Creutzfeldt-Jacob (MCJ).- Le syndrome de Gerstmann-Sträussler-Scheinker (SGSS).- L'insomnie fatale familiale (IFF).- La paraparésie spastique (PS).- Le prion.- Historique.- Les aspects génétiques.- Les aspects biochimiques.- Les fonctions biologiques de la prion-protéine.- La diversité des prions : les diverses "souches".- Essai de synthèse : les théories du prion.- Les risques de transmission accidentelles des maladies à prion.- Précautions à prendre et recommandations.- Les essais thérapeutiques.- Conclusion.

Keywords

Semiology. Diagnosis. Symptomatology --- Animaux [Maladies à prions chez les ] --- BSE (Disease) --- BSE (Maladie) --- BSE (Ziekte) --- Besmettelijke ziekten --- Besmettelijke ziekten bij dieren --- Bovine spongiform encephalopathy --- CJD (Disease) --- Communicable diseases --- Communicable diseases between animals and man --- Communicable diseases in animals --- Contagion and contagious diseases --- Contagious diseases --- Creutzfeldt-Jakob [Ziekte van ] --- Creutzfeldt-Jakob disease --- Creutzfeldt-Jakob syndrome --- Dieren [Prionziekten bij de ] --- Dierenepidemieen --- Encepholopathies [Spongiform ] --- Encéphalopathie spongiforme --- Encéphalopathie spongiforme bovine --- Epidemieen bij dieren --- Epidemies chez les animaux --- Epizootic diseases --- Epizootieen --- Epizooties --- Gekkekoeienziekte --- Heidenhain syndrome --- Infectious diseases --- Infectious protein particles --- Jakob's disease --- Jakob-Creutzfeldt disease --- Jakob-Creutzfeldt syndrome --- Jakob-Creutzfeldt-ziekte --- Kourou --- Kuru --- Maladie de Creutzfeldt-Jakob --- Maladie de la mort souriante --- Maladie de la vache folle --- Maladie des vaches folles --- Maladies contagieuses --- Maladies contagieuses chez les animaux --- Maladies contagieuses entre les animaux et l'homme --- Maladies microbiennes des animaux --- Maladies à prions --- Maladies à prions chez les animaux --- Microbial diseases in animals --- Microbial diseases in man --- Microbiele ziekten van de dieren --- Overdraagbare ziekten tussen dier en mens --- Prion diseases --- Prion diseases in animals --- Prion infections --- Prions --- Prions [Maladies à ] --- Prionziekten --- Prionziekten bij de dieren --- Protein particles [Infectious ] --- Spastic pseudosclerosis --- Spongiform encephalopathies --- Spongiform encephalopathy --- Spongiform encephalopathy [Bovine ] --- Spongiforme encefalopathie --- Sub-acute spongiform encephalopathy --- Subacute spongoform encephalopathy --- Transmissible spongiform encephalopathies --- Unconventional slow virus diseases --- Vache folle [Maladie de la ] --- Vaches folles [Maladies des ] --- Ziekten [Besmettelijke ] --- Ziekten [Prion] --- Zoonoses --- Zoonotic diseases --- Zoönosen --- Zymotic diseases --- Prion diseases. --- Creutzfeldt-Jakob disease. --- Prion Diseases. --- Creutzfeldt-Jakob Syndrome. --- Encephalopathies, Spongiform --- Subacute spongiform encephalopathy --- Slow virus diseases --- Central nervous system --- Presenile dementia --- Diseases --- Creutzfeldt-Jakob Syndrome --- Encephalopathy, Bovine Spongiform --- Encephalopathy, Bovine Spongiform.

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