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Huntington's disease (HD) is an inherited progressive neurodegenerative disorder. Although onset of Huntington's Disease usually occurs in adulthood, the age of onset of the condition is extremely variable with approximately 5-10% of cases having an onset of less than 20 years, or Juvenile Huntington's Disease (JHD). While JHD shares many of the clinical features of adult HD (e.g., chorea and personality disorders), patients with JHD often experience additional problems includingseizures, dystonia and Parkinsonism. Diagnosis in patients with JHD is often delayed because of the failure of clini

Huntington's chorea. --- Genetic disorders in children. --- Trinucleotide repeats. --- Repeats, Trinucleotide --- Repeats, Triplet (Nucleotides) --- Triplet repeats (Nucleotides) --- Microsatellites (Genetics) --- Nucleotides --- Children --- Chronic progressive chorea --- Chronic progressive hereditary chorea --- Degenerative chorea --- HC (Disease) --- HD (Disease) --- Hereditary chorea --- Huntington chorea --- Huntington chronic progressive hereditary chorea --- Huntington disease --- Huntington's chorea --- Lund-Huntington chorea --- Microcellular striatal syndrome --- Progressive hereditary chorea, Chronic --- Chorea --- Dementia --- Genetic disorders --- Nervous system --- Diseases --- Genetic aspects --- Degeneration --- Adolescent. --- Child. --- Huntington Disease. --- Trinucleotide Repeat Expansion. --- Huntington's disease .